Sputum culture grew Klebsiella pneumoniae.Ĭhest x-ray revealed dextrocardia, bronchial wall thickening, fibrosis and cystic changes in right lower zone and left lower zone. Routine biochemical tests including liver, renal function tests were normal. There was no evidence of pulmonary hypertension clinically.ĬBC revealed normal counts, PCV was not raised. Heart sounds were best heard on right side. Cardiovascular examination revealed dextrocardia with apex impulse on right side. On examination of the respiratory system, medium-coarse crackles in infra-axillary, infrascapular areas were bilaterally present. There was no clubbing, cyanosis, pallor, icterus, lymphadenopathy, edema feet, or raised JVP. On examination, she was mildly breathless but otherwise in good health.
Neither was there history of hospitalization, nor anytime had she come under institutional medical care. There was no history of hemoptysis, pedal edema and paroxysmal nocturnal dyspnoea. On enquiry, she revealed that she was also suffering from hearing loss. As Kartagener described this syndrome in detail, it bears his name.Ī 60 year old female from interior rural Maharashtra presented to our institute with productive cough and dyspnea for the last 8 to10 years. Manes Kartagener first recognized this clinical triad as a distinct congenital syndrome in 1933. Zivert first described the combination of situs inversus, chronic sinusitis, and bronchiectasis in 1904. It is also known as Afzelius syndrome, Kartagener's triad, Zivert's syndrome, or Zivert-Kartagener triad. It is characterized by a triad of situs inversus of the viscera, sinusitis, bronchiectasis, and ciliary dysfunction. Kartagener's syndrome (KS) is a ciliopathic, autosomal recessive disorder that causes a defect in the action of the cilia lining the respiratory tract and Fallopian tube More Details.
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How to cite this URL: Potdar PV, Nayak MM, Chitnis A.
How to cite this article: Potdar PV, Nayak MM, Chitnis A. Keywords: Kartagener′s syndrome, primary ciliary dyskinesia, situs inversus We report a case of Kartagener's syndrome in a female patient diagnosed in her sixties. In majority of adult patients, bronchiectasis follows necrotizing infection. In patients presenting in middle or old age with bronchiectasis, congenital and hereditary causes of bronchiectasis are not commonly encountered. Bronchiectasis may have varied etiologies.
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